From: Streptococcus pyogenes-purpura fulminans as an invasive form of group A streptococcal infection
Patient no | Sex | Age at onset | Underlying disease | Plasma activity of protein C (%) | Complications | Outcomes | Reports | ||
---|---|---|---|---|---|---|---|---|---|
Extremities | Neurological | ||||||||
1 | M | 2 months | No | NR | Shock, DIC | Death | NR | Death | Lloyd and Bolte [14] |
2 | M | 4 months | No | 6 | Shock, DIC | Alive | All toes and 7 digits lost | No deficits | Dhodapkar et al. [15] |
3 | F | 2.5 years | No | NR | Shock, DIC, ARDS, MOF | Alive | Preserved | Brain death | Daskalaki et al. [16] |
4 | M | 3 years | No | 13 | Shock, DIC | Alive | Amputation | No deficits | Our case |
5 | M | 5 years | No | 60 | Shock, DIC | Alive | Preserved | No deficits | Dhodapkar et al. [15] |
6 | M | 7 years | No | NR | Shock, DIC | Alive | Amputation | NR | Davis et al. [17] |
7 | F | 7 years | Chylothorax | NR | Shock, DIC, MOF | Alive | Amputation | NR | Cruz et al. [18] |
8 | F | 8 years | JIA, TNFα-blocker | NR | Shock, DIC, Renal failure | Death | Amputation | Death | Renaud et al. [19] |
9 | F | 10 years | JIA, TNFα-blocker | NR | Shock, DIC, ARDS | Alive | Amputation | NR | Lovell et al. [20] |
10 | M | 50 years | No | Normal | Shock, DIC, Renal failure | Alive | Skin grafting | NR | Gupta [21] |
11 | F | 62 years | Asplenia, NHL | NR | DIC | Death | NR | Death | Ward et al. [22] |
12 | F | 72 years | No | NR | Shock, DIC | Alive | NR | NR | Ashokkumar et al. [23] |